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Congenital hepatic fibrosis and coexistent retinal macular degeneration: A case report

RATIONALE: Congenital hepatic fibrosis (CHF) is an autosomal recessive disease characterized by periportal fibrosis, portal hypertension, and renal cystic disease. Essentially, CHF is a variant of fibrocystic disorder in which liver and kidney are commonly affected. Other frequently associated condi...

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Detalhes bibliográficos
Publicado no:Medicine (Baltimore)
Main Authors: Li, Dezhao, Qin, Junjie, Sun, Shijuan, Li, Xu
Formato: Artigo
Idioma:Inglês
Publicado em: Wolters Kluwer Health 2019
Assuntos:
Acesso em linha:https://ncbi.nlm.nih.gov/pmc/articles/PMC6736369/
https://ncbi.nlm.nih.gov/pubmed/31464924
https://ncbi.nlm.nih.govhttp://dx.doi.org/10.1097/MD.0000000000016909
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