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Cellular and Molecular Mechanisms in the Pathogenesis of Classical, Vascular, and Hypermobile Ehlers‒Danlos Syndromes

The Ehlers‒Danlos syndromes (EDS) constitute a heterogenous group of connective tissue disorders characterized by joint hypermobility, skin abnormalities, and vascular fragility. The latest nosology recognizes 13 types caused by pathogenic variants in genes encoding collagens and other molecules inv...

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Detalles Bibliográficos
Publicado en:Genes (Basel)
Main Authors: Chiarelli, Nicola, Ritelli, Marco, Zoppi, Nicoletta, Colombi, Marina
Formato: Artigo
Idioma:Inglês
Publicado: MDPI 2019
Assuntos:
Acceso en liña:https://ncbi.nlm.nih.gov/pmc/articles/PMC6723307/
https://ncbi.nlm.nih.gov/pubmed/31409039
https://ncbi.nlm.nih.govhttp://dx.doi.org/10.3390/genes10080609
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