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Clinicoradiological Spectrum of L-2-Hydroxy Glutaric Aciduria: Typical and Atypical Findings in an Indian Cohort

CONTEXT: Neurometabolic disorders form an important group of potentially treatable diseases. It is important to recognize the clinical phenotype and characteristic imaging patterns to make an early diagnosis and initiate appropriate treatment. L-2-hydroxy glutaric aciduria (L2HGA) is a rare organic...

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Publicado en:J Clin Imaging Sci
Autores principales: Muthusamy, Karthik, Sudhakar, Sniya Valsa, Christudass, Christhunesa S, Chandran, Mahalakshmi, Thomas, Maya, Gibikote, Sridhar
Formato: Artigo
Lenguaje:Inglês
Publicado: Scientific Scholar 2019
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Acceso en línea:https://ncbi.nlm.nih.gov/pmc/articles/PMC6702895/
https://ncbi.nlm.nih.gov/pubmed/31448154
https://ncbi.nlm.nih.govhttp://dx.doi.org/10.25259/JCIS-9-3
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