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Twenty-four-Hour Motor Activity and Body Temperature Patterns Suggest Altered Central Circadian Timekeeping in Smith-Magenis Syndrome, a Neurodevelopmental Disorder

Smith-Magenis Syndrome (SMS) is a contiguous gene syndrome linked to interstitial microdeletion, or mutation of RAI1, within chromosome 17p11.2. Key behavioral features of SMS include intellectual disability (ID), sleep-disturbances, maladaptive, aggressive and self-injurious behaviors, hyperactivit...

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Pubblicato in:Am J Med Genet A
Autori principali: Smith, Ann C.M., Morse, Rebecca S., Introne, Wendy, Duncan, Wallace C.
Natura: Artigo
Lingua:Inglês
Pubblicazione: 2019
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Accesso online:https://ncbi.nlm.nih.gov/pmc/articles/PMC6699156/
https://ncbi.nlm.nih.gov/pubmed/30690916
https://ncbi.nlm.nih.govhttp://dx.doi.org/10.1002/ajmg.a.61003
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