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A null allele of Dnaaf2 displays embryonic lethality and mimics human ciliary dyskinesia

The dynein axonemal assembly factor (Dnaaf) protein family is involved in preassembly and stability of dynein arms before they are transported into the cilia. In humans, mutations in DNAAF genes lead to several diseases related to cilia defects such as primary ciliary dyskinesia (PCD; OMIM: 612518)....

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Detalhes bibliográficos
Publicado no:Hum Mol Genet
Main Authors: Cheong, Agnes, Degani, Rinat, Tremblay, Kimberly D, Mager, Jesse
Formato: Artigo
Idioma:Inglês
Publicado em: Oxford University Press 2019
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Acesso em linha:https://ncbi.nlm.nih.gov/pmc/articles/PMC6688062/
https://ncbi.nlm.nih.gov/pubmed/31107948
https://ncbi.nlm.nih.govhttp://dx.doi.org/10.1093/hmg/ddz106
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