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Rosai - Dorfman disease: a rare entity diagnosed at autopsy

Rosai-Dorfman disease (RDD) or Sinus histiocytosis with massive lymphadenopathy is a rare and benign histiocytic proliferative disorder first described by Juan Rosai and Ronald Dorfman in 1969, whose etiology remains unknown. Since then, many cases were reported in the literature. The disease primar...

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Publicado en:Autops Case Rep
Autores principales: Veloso, João da Costa, Siqueira, Sheila Aparecida Coelho, Zerbini, Maria Claudia Nogueira
Formato: Artigo
Lenguaje:Inglês
Publicado: São Paulo, SP: Universidade de São Paulo, Hospital Universitário 2013
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Acceso en línea:https://ncbi.nlm.nih.gov/pmc/articles/PMC6671884/
https://ncbi.nlm.nih.gov/pubmed/31528594
https://ncbi.nlm.nih.govhttp://dx.doi.org/10.4322/acr.2013.004
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