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Functional Characterization of Rab7 Mutant Proteins Associated with Charcot-Marie-Tooth Type 2B Disease

Charcot-Marie-Tooth (CMT) type 2 neuropathies are a group of autosomal-dominant axonal disorders genetically and clinically heterogeneous. In particular, CMT type 2B (CMT2B) neuropathies are characterized by severe sensory loss, often complicated by infections, arthropathy, and amputations. Recently...

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Dades bibliogràfiques
Publicat a:J Neurosci
Autors principals: Spinosa, Maria Rita, Progida, Cinzia, De Luca, Azzurra, Colucci, Anna Maria Rosaria, Alifano, Pietro, Bucci, Cecilia
Format: Artigo
Idioma:Inglês
Publicat: Society for Neuroscience 2008
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Accés en línia:https://ncbi.nlm.nih.gov/pmc/articles/PMC6671532/
https://ncbi.nlm.nih.gov/pubmed/18272684
https://ncbi.nlm.nih.govhttp://dx.doi.org/10.1523/JNEUROSCI.3677-07.2008
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