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Loss of base-to-apex circumferential strain gradient assessed by cardiovascular magnetic resonance in Fabry disease: relationship to T1 mapping, late gadolinium enhancement and hypertrophy

BACKGROUND: Cardiac involvement is common and is the leading cause of mortality in Fabry disease (FD). We explored the association between cardiovascular magnetic resonance (CMR) myocardial strain, T1 mapping, late gadolinium enhancement (LGE) and left ventricular hypertrophy (LVH) in patients with...

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Pubblicato in:J Cardiovasc Magn Reson
Autori principali: Mathur, Shobhit, Dreisbach, John G., Karur, Gauri R., Iwanochko, Robert M., Morel, Chantal F., Wasim, Syed, Nguyen, Elsie T., Wintersperger, Bernd J., Hanneman, Kate
Natura: Artigo
Lingua:Inglês
Pubblicazione: BioMed Central 2019
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Accesso online:https://ncbi.nlm.nih.gov/pmc/articles/PMC6670217/
https://ncbi.nlm.nih.gov/pubmed/31366357
https://ncbi.nlm.nih.govhttp://dx.doi.org/10.1186/s12968-019-0557-0
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