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Neutrophil activation in systemic capillary leak syndrome (Clarkson disease)

Systemic capillary leak syndrome (SCLS; Clarkson disease) is a rare orphan disorder characterized by transient yet recurrent episodes of hypotension and peripheral oedema due to diffuse vascular leakage of fluids and proteins into soft tissues. Humoral mediators, cellular responses and genetic featu...

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Dades bibliogràfiques
Publicat a:J Cell Mol Med
Autors principals: Xie, Zhihui, Kuhns, Douglas B., Gu, Xuesong, Otu, Hasan H., Libermann, Towia A., Gallin, John I., Parikh, Samir M., Druey, Kirk M.
Format: Artigo
Idioma:Inglês
Publicat: John Wiley and Sons Inc. 2019
Matèries:
Accés en línia:https://ncbi.nlm.nih.gov/pmc/articles/PMC6653644/
https://ncbi.nlm.nih.gov/pubmed/31210423
https://ncbi.nlm.nih.govhttp://dx.doi.org/10.1111/jcmm.14381
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