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Pulmonary Arterial Hypertension Due to NPR-C Mutation: A Novel Paradigm for Normal and Pathologic Remodeling?

Idiopathic Pulmonary Arterial Hypertension (IPAH) is a deadly and disabling disease characterized by severe vascular remodeling of small pulmonary vessels by fibroblasts, myofibroblasts and vascular smooth muscle cell proliferation. Recent studies suggest that the Natriuretic Peptide Clearance Recep...

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Detaylı Bibliyografya
Yayımlandı:Int J Mol Sci
Yazar: Egom, Emmanuel Eroume-A
Materyal Türü: Artigo
Dil:Inglês
Baskı/Yayın Bilgisi: MDPI 2019
Konular:
Online Erişim:https://ncbi.nlm.nih.gov/pmc/articles/PMC6628360/
https://ncbi.nlm.nih.gov/pubmed/31234560
https://ncbi.nlm.nih.govhttp://dx.doi.org/10.3390/ijms20123063
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