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Lymphangioleiomyomatosis manifesting as refractory chylothorax and chyloperitoneum

This is a rare case of sporadic lymphangioleiomyomatosis (S-LAM) manifesting as refractory chylothorax and chyloperitoneum. A middle-aged woman with unremarkable medical history presented with respiratory failure, abdominal distension and anasarca. She was found to have high-output chylous effusion...

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Pubblicato in:BMJ Case Rep
Autori principali: Chen, Yee-Shiuan, Memon, Pauras
Natura: Artigo
Lingua:Inglês
Pubblicazione: BMJ Publishing Group 2019
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Accesso online:https://ncbi.nlm.nih.gov/pmc/articles/PMC6626491/
https://ncbi.nlm.nih.gov/pubmed/31300601
https://ncbi.nlm.nih.govhttp://dx.doi.org/10.1136/bcr-2019-229958
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