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Low-dose sirolimus in retroperitoneal lymphangioleiomyomas

Lymphangioleiomyomatosis (LAM) is a rare disease associated with cystic lung destruction and abdominal tumors, including lymphangioleiomyomas, which frequently occur in the retroperitoneal region. Sirolimus therapy is currently recommended for LAM patients with abnormal or declining lung function wi...

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Dades bibliogràfiques
Publicat a:Lung India
Autors principals: Ussavarungsi, Kamonpun, Laroia, Archana T, Burger, Charles D
Format: Artigo
Idioma:Inglês
Publicat: Wolters Kluwer - Medknow 2019
Matèries:
Accés en línia:https://ncbi.nlm.nih.gov/pmc/articles/PMC6625232/
https://ncbi.nlm.nih.gov/pubmed/31290423
https://ncbi.nlm.nih.govhttp://dx.doi.org/10.4103/lungindia.lungindia_433_18
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