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Disrupted Plasma Membrane Protein Homeostasis in a Xenopus Laevis Model of Retinitis Pigmentosa

Rhodopsin mislocalization is frequently observed in retinitis pigmentosa (RP) patients. For example, class I mutant rhodopsin is deficient in the VxPx trafficking signal, mislocalizes to the plasma membrane (PM) of rod photoreceptor inner segments (ISs), and causes autosomal dominant RP. Mislocalize...

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Wedi'i Gadw mewn:
Manylion Llyfryddiaeth
Cyhoeddwyd yn:J Neurosci
Prif Awduron: Ropelewski, Philip, Imanishi, Yoshikazu
Fformat: Artigo
Iaith:Inglês
Cyhoeddwyd: Society for Neuroscience 2019
Pynciau:
Mynediad Ar-lein:https://ncbi.nlm.nih.gov/pmc/articles/PMC6616295/
https://ncbi.nlm.nih.gov/pubmed/31061086
https://ncbi.nlm.nih.govhttp://dx.doi.org/10.1523/JNEUROSCI.3025-18.2019
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