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Polycystic kidney disease

Cystic kidneys are common causes of end-stage renal disease, both in children and in adults. Autosomal dominant polycystic kidney disease (ADPKD) and autosomal recessive polycystic kidney disease (ARPKD) are cilia-related disorders and the two main forms of monogenic cystic kidney diseases. ADPKD is...

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Dettagli Bibliografici
Pubblicato in:Nat Rev Dis Primers
Autori principali: Bergmann, Carsten, Guay-Woodford, Lisa M., Harris, Peter C., Horie, Shigeo, Peters, Dorien J. M., Torres, Vicente E.
Natura: Artigo
Lingua:Inglês
Pubblicazione: 2018
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Accesso online:https://ncbi.nlm.nih.gov/pmc/articles/PMC6592047/
https://ncbi.nlm.nih.gov/pubmed/30523303
https://ncbi.nlm.nih.govhttp://dx.doi.org/10.1038/s41572-018-0047-y
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