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Paroxysmal Nocturnal Hemoglobinuria: Diagnostic Challenges in Pediatric Patient

Paroxysmal nocturnal hemoglobinuria (PNH) is a rare, life-threatening hematologic stem cell disorder characterized by hemoglobinuria, thrombosis, and tendency for bone marrow failure. The rare incidence of PNH in children, its nonspecific clinical presentation, and occasional absence of hemoglobinur...

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Wedi'i Gadw mewn:
Manylion Llyfryddiaeth
Cyhoeddwyd yn:Case Rep Pediatr
Prif Awduron: Krishnaprasadh, Dharshana, Kaminecki, Inna, Sechser Perl, Anna, Teitelbaum, Jonathan
Fformat: Artigo
Iaith:Inglês
Cyhoeddwyd: Hindawi 2019
Pynciau:
Mynediad Ar-lein:https://ncbi.nlm.nih.gov/pmc/articles/PMC6590537/
https://ncbi.nlm.nih.gov/pubmed/31281702
https://ncbi.nlm.nih.govhttp://dx.doi.org/10.1155/2019/4930494
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