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Network Biology Identifies Novel Regulators of CFTR Trafficking and Membrane Stability

In cystic fibrosis, the most common disease-causing mutation is F508del, which causes not only intracellular retention and degradation of CFTR, but also defective channel gating and decreased membrane stability of the small amount that reaches the plasma membrane (PM). Thus, pharmacological correcti...

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Dettagli Bibliografici
Pubblicato in:Front Pharmacol
Autori principali: Loureiro, Cláudia Almeida, Santos, João D., Matos, Ana Margarida, Jordan, Peter, Matos, Paulo, Farinha, Carlos M., Pinto, Francisco R.
Natura: Artigo
Lingua:Inglês
Pubblicazione: Frontiers Media S.A. 2019
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Accesso online:https://ncbi.nlm.nih.gov/pmc/articles/PMC6559121/
https://ncbi.nlm.nih.gov/pubmed/31231217
https://ncbi.nlm.nih.govhttp://dx.doi.org/10.3389/fphar.2019.00619
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