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Systemic Epstein–Barr Virus-Positive T/NK Lymphoproliferative Diseases With SH2D1A/XIAP Hypomorphic Gene Variants

X-linked lymphoproliferative disease (XLP) is one of the X-linked primary immunodeficiency diseases (PIDs) with defective immune response to Epstein–Barr virus (EBV) infection. Chronic active EBV infection (CAEBV) and EBV-hemophagocytic lymphohistiocytosis (HLH) are recognized as systemic EBV-positi...

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書目詳細資料
發表在:Front Pediatr
Main Authors: Ishimura, Masataka, Eguchi, Katsuhide, Shiraishi, Akira, Sonoda, Motoshi, Azuma, Yoshihiro, Yamamoto, Hiroyuki, Imadome, Ken-ichi, Ohga, Shouichi
格式: Artigo
語言:Inglês
出版: Frontiers Media S.A. 2019
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在線閱讀:https://ncbi.nlm.nih.gov/pmc/articles/PMC6558365/
https://ncbi.nlm.nih.gov/pubmed/31231620
https://ncbi.nlm.nih.govhttp://dx.doi.org/10.3389/fped.2019.00183
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