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SUN-274 Unusual Case of Beckwith Weidemann Syndrome with Spontaneous Resolution of a Hepatic Mass

Background: Beckwith-Wiedemann Syndrome (BWS) is an overgrowth syndrome with risk for embryonal tumors (8-10%) like Wilms tumor, hepatoblastoma, adrenal carcinoma and neuroblastoma. Benign tumors like hemangiomas (HM) and hamartomas have rarely been reported. Over expression of paternal growth promo...

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Detalles Bibliográficos
Publicado en:J Endocr Soc
Main Authors: Sodhi, Misha, Kubhar, Dineeta, Mehta, Shilpa, Yachelevich, Naomi, Chang, Lucy, Shah, Bina
Formato: Artigo
Idioma:Inglês
Publicado: Endocrine Society 2019
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Acceso en liña:https://ncbi.nlm.nih.gov/pmc/articles/PMC6553157/
https://ncbi.nlm.nih.govhttp://dx.doi.org/10.1210/js.2019-SUN-274
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