Caricamento...

Hearing Dysfunction in a Large Family Affected by Dominant Optic Atrophy (OPA8-Related DOA): A Human Model of Hidden Auditory Neuropathy

Hidden auditory neuropathy is characterized by reduced performances in challenging auditory tasks with the preservation of hearing thresholds, resulting from diffuse loss of cochlear inner hair cell (IHC) synapses following primary degeneration of unmyelinated terminals of auditory fibers. We report...

Descrizione completa

Salvato in:
Dettagli Bibliografici
Pubblicato in:Front Neurosci
Autori principali: Santarelli, Rosamaria, La Morgia, Chiara, Valentino, Maria Lucia, Barboni, Piero, Monteleone, Anna, Scimemi, Pietro, Carelli, Valerio
Natura: Artigo
Lingua:Inglês
Pubblicazione: Frontiers Media S.A. 2019
Soggetti:
Accesso online:https://ncbi.nlm.nih.gov/pmc/articles/PMC6546873/
https://ncbi.nlm.nih.gov/pubmed/31191217
https://ncbi.nlm.nih.govhttp://dx.doi.org/10.3389/fnins.2019.00501
Tags: Aggiungi Tag
Nessun Tag, puoi essere il primo ad aggiungerne! !