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Triheptanoin versus trioctanoin for long-chain fatty acid oxidation disorders: a double blinded, randomized controlled trial

BACKGROUND: Observational reports suggest that supplementation that increases citric acid cycle intermediates via anaplerosis may have therapeutic advantages over traditional medium-chain triglyceride (MCT) treatment of long-chain fatty acid oxidation disorders (LC-FAODs) but controlled trials have...

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Detalhes bibliográficos
Publicado no:J Inherit Metab Dis
Main Authors: Gillingham, Melanie B., Heitner, Stephen B., Martin, Julie, Rose, Sarah, Goldstein, Amy, El-Gharbawy, Areeg Hassan, Deward, Stephanie, Lasarev, Michael R., Pollaro, Jim, DeLany, James P., Burchill, Luke J., Goodpaster, Bret, Shoemaker, James, Matern, Dietrich, Harding, Cary O., Vockley, Jerry
Formato: Artigo
Idioma:Inglês
Publicado em: 2017
Assuntos:
Acesso em linha:https://ncbi.nlm.nih.gov/pmc/articles/PMC6545116/
https://ncbi.nlm.nih.gov/pubmed/28871440
https://ncbi.nlm.nih.govhttp://dx.doi.org/10.1007/s10545-017-0085-8
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