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Biochemical Markers for the Diagnosis and Monitoring of Wilson Disease

Wilson disease (WD) is an autosomal recessively-inherited disorder of copper metabolism and characterised by a pathological accumulation of copper. The ATP7B gene encodes for a transmembrane copper transporter essential for biliary copper excretion. Depending on time of diagnosis, severity of diseas...

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Publicat a:Clin Biochem Rev
Autors principals: Mohr, Isabelle, Weiss, Karl Heinz
Format: Artigo
Idioma:Inglês
Publicat: The Australian Association of Clinical Biochemists 2019
Matèries:
Accés en línia:https://ncbi.nlm.nih.gov/pmc/articles/PMC6544250/
https://ncbi.nlm.nih.gov/pubmed/31205375
https://ncbi.nlm.nih.govhttp://dx.doi.org/10.33176/AACB-18-00014
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