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Linear IgA bullous dermatosis in adults and children: a clinical and immunopathological study of 38 patients

BACKGROUND: Linear IgA bullous dermatosis (LABD) is a rare autoimmune subepithelial vesiculobullous disease due to IgA autoantibodies directed against different antigens of the basement membrane zone (BMZ) of the skin and/or mucosae. It affects mainly preschool-aged children and adults, with only fe...

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Dades bibliogràfiques
Publicat a:Orphanet J Rare Dis
Autors principals: Genovese, Giovanni, Venegoni, Luigia, Fanoni, Daniele, Muratori, Simona, Berti, Emilio, Marzano, Angelo Valerio
Format: Artigo
Idioma:Inglês
Publicat: BioMed Central 2019
Matèries:
Accés en línia:https://ncbi.nlm.nih.gov/pmc/articles/PMC6534856/
https://ncbi.nlm.nih.gov/pubmed/31126328
https://ncbi.nlm.nih.govhttp://dx.doi.org/10.1186/s13023-019-1089-2
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