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Therapeutic plasma exchange in familial hemophagocytic lymphohistiocytosis
Familial hemophagocytic lymphohistiocytosis is a rare, life-threatening disorder characterized by impaired cytotoxicity, hypercytokinemia and immune-mediated organ injury. We report a 7-week-old male of consanguineous parents who presented with fever, pancytopenia and multi-organ failure. Elevated i...
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| Publicado no: | J Pediatr Intensive Care |
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| Main Authors: | , , , , , |
| Formato: | Artigo |
| Idioma: | Inglês |
| Publicado em: |
Georg Thieme Verlag KG
2014
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| Acesso em linha: | https://ncbi.nlm.nih.gov/pmc/articles/PMC6530735/ https://ncbi.nlm.nih.gov/pubmed/31214450 https://ncbi.nlm.nih.govhttp://dx.doi.org/10.3233/PIC-14079 |
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