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Therapeutic plasma exchange in familial hemophagocytic lymphohistiocytosis

Familial hemophagocytic lymphohistiocytosis is a rare, life-threatening disorder characterized by impaired cytotoxicity, hypercytokinemia and immune-mediated organ injury. We report a 7-week-old male of consanguineous parents who presented with fever, pancytopenia and multi-organ failure. Elevated i...

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Publicat a:J Pediatr Intensive Care
Autors principals: Edwards-Richards, Alcia, Defreitas, Marissa, Katsoufis, Chryso, Jeyapalan, Asumthia, Nares, Michael, Abitbol, Carolyn L.
Format: Artigo
Idioma:Inglês
Publicat: Georg Thieme Verlag KG 2014
Accés en línia:https://ncbi.nlm.nih.gov/pmc/articles/PMC6530735/
https://ncbi.nlm.nih.gov/pubmed/31214450
https://ncbi.nlm.nih.govhttp://dx.doi.org/10.3233/PIC-14079
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