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Genetic Causes of Surfactant Protein Abnormalities

PURPOSE OF REVIEW: Mutations in genes encoding proteins critical for the production and function of pulmonary surfactant cause diffuse lung disease. Timely recognition and diagnosis of affected individuals is important for proper counseling concerning prognosis and recurrence risk. RECENT FINDINGS:...

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Detalles Bibliográficos
Publicado en:Curr Opin Pediatr
Autor Principal: Nogee, Lawrence M.
Formato: Artigo
Idioma:Inglês
Publicado: 2019
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Acceso en liña:https://ncbi.nlm.nih.gov/pmc/articles/PMC6530488/
https://ncbi.nlm.nih.gov/pubmed/31090574
https://ncbi.nlm.nih.govhttp://dx.doi.org/10.1097/MOP.0000000000000751
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