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Combined Phenotypes of Spondylometaphyseal Dysplasia-Kozlowski Type and Charcot-Marie-Tooth Disease Type 2C Secondary to a TRPV4 Pathogenic Variant

TRPV4, a nonselective calcium permeable ion channel, is expressed broadly in many organs including bone and neurons. Pathogenic variants in TRPV4 are known to cause both a spectrum of skeletal dysplasias and neuropathies. Recent publications have documented a few patients who have a combined phenoty...

Ausführliche Beschreibung

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Bibliographische Detailangaben
Veröffentlicht in:Mol Syndromol
Hauptverfasser: Faye, Eden, Modaff, Peggy, Pauli, Richard, Legare, Janet
Format: Artigo
Sprache:Inglês
Veröffentlicht: S. Karger AG 2019
Schlagworte:
Online Zugang:https://ncbi.nlm.nih.gov/pmc/articles/PMC6528083/
https://ncbi.nlm.nih.gov/pubmed/31191204
https://ncbi.nlm.nih.govhttp://dx.doi.org/10.1159/000495778
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