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Mitochondrial Genetic Disorders: Cell Signaling and Pharmacological Therapies
Mitochondrial fatty acid oxidation (FAO) and respiratory chain (RC) defects form a large group of inherited monogenic disorders sharing many common clinical and pathophysiological features, including disruption of mitochondrial bioenergetics, but also, for example, oxidative stress and accumulation...
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| Publicado no: | Cells |
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| Main Authors: | , |
| Formato: | Artigo |
| Idioma: | Inglês |
| Publicado em: |
MDPI
2019
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| Assuntos: | |
| Acesso em linha: | https://ncbi.nlm.nih.gov/pmc/articles/PMC6523966/ https://ncbi.nlm.nih.gov/pubmed/30925787 https://ncbi.nlm.nih.govhttp://dx.doi.org/10.3390/cells8040289 |
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