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A148 SIROLIMUS FOR PRIMARY INTESTINAL LYMPHANGIECTASIA IN A PEDIATRIC PATIENT

BACKGROUND: Primary intestinal lymphangiectasia (PIL) is a rare digestive disorder characterized by morphologic abnormalities in the intestinal lymphatics resulting in protein losing enteropathy (PLE). PIL usually presents early in childhood with persistent diarrhea, peripheral edema and ascites. Di...

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Detalles Bibliográficos
Publicado en:J Can Assoc Gastroenterol
Main Authors: Strauss, J, Gidrewicz, D, McKenzie, L
Formato: Artigo
Idioma:Inglês
Publicado: Oxford University Press 2019
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Acceso en liña:https://ncbi.nlm.nih.gov/pmc/articles/PMC6512539/
https://ncbi.nlm.nih.govhttp://dx.doi.org/10.1093/jcag/gwz006.147
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