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Myocardial fibrosis by late gadolinium enhancement cardiovascular magnetic resonance in myotonic muscular dystrophy type 1: highly prevalent but not associated with surface conduction abnormality

BACKGROUND: Conduction disease and arrhythmias represent a major cause of mortality in myotonic muscular dystrophy type 1 (MMD1). Permanent pacemaker (PPM) implantation is the cornerstone of therapy to reduce cardiovascular mortality in MMD1. Cardiovascular magnetic resonance (CMR) studies demonstra...

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Dades bibliogràfiques
Publicat a:J Cardiovasc Magn Reson
Autors principals: Cardona, Andrea, Arnold, William D., Kissel, John T., Raman, Subha V., Zareba, Karolina M.
Format: Artigo
Idioma:Inglês
Publicat: BioMed Central 2019
Matèries:
Accés en línia:https://ncbi.nlm.nih.gov/pmc/articles/PMC6498496/
https://ncbi.nlm.nih.gov/pubmed/31046780
https://ncbi.nlm.nih.govhttp://dx.doi.org/10.1186/s12968-019-0535-6
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