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Metabolic disease and ABHD6 alter the circulating bis(monoacylglycerol)phosphate profile in mice and humans

Bis(monoacylglycerol)phosphate (BMP) is a phospholipid that is crucial for lipid degradation and sorting in acidic organelles. Genetic and drug-induced lysosomal storage disorders (LSDs) are associated with increased BMP concentrations in tissues and in the circulation. Data on BMP in disorders othe...

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Dades bibliogràfiques
Publicat a:J Lipid Res
Autors principals: Grabner, Gernot F., Fawzy, Nermeen, Pribasnig, Maria A., Trieb, Markus, Taschler, Ulrike, Holzer, Michael, Schweiger, Martina, Wolinski, Heimo, Kolb, Dagmar, Horvath, Angela, Breinbauer, Rolf, Rülicke, Thomas, Rabl, Roland, Lass, Achim, Stadlbauer, Vanessa, Hutter-Paier, Birgit, Stauber, Rudolf E., Fickert, Peter, Zechner, Rudolf, Marsche, Gunther, Eichmann, Thomas O., Zimmermann, Robert
Format: Artigo
Idioma:Inglês
Publicat: The American Society for Biochemistry and Molecular Biology 2019
Matèries:
Accés en línia:https://ncbi.nlm.nih.gov/pmc/articles/PMC6495172/
https://ncbi.nlm.nih.gov/pubmed/30894461
https://ncbi.nlm.nih.govhttp://dx.doi.org/10.1194/jlr.M093351
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