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Erythropoietin and Friedreich Ataxia: Time for a Reappraisal?

Friedreich ataxia (FRDA) is a rare neurological disorder due to deficiency of the mitochondrial protein frataxin. Frataxin deficiency results in impaired mitochondrial function and iron deposition in affected tissues. Erythropoietin (EPO) is a cytokine which was mostly known as a key regulator of er...

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Detalles Bibliográficos
Publicado en:Front Neurosci
Main Authors: Boesch, Sylvia, Indelicato, Elisabetta
Formato: Artigo
Idioma:Inglês
Publicado: Frontiers Media S.A. 2019
Assuntos:
Acceso en liña:https://ncbi.nlm.nih.gov/pmc/articles/PMC6491891/
https://ncbi.nlm.nih.gov/pubmed/31105516
https://ncbi.nlm.nih.govhttp://dx.doi.org/10.3389/fnins.2019.00386
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