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Angiotensin-converting enzyme inhibitors may affect pulmonary function in lymphangioleiomyomatosis
INTRODUCTION. A local renin-angiotensin system exists in the pulmonary nodules of lymphangioleiomyomatosis patients. Sirolimus, the standard treatment for lymphangioleiomyomatosis, stabilizes lung function, but all patients do not respond to or tolerate sirolimus. As renin-angiotensin systems may af...
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| Опубликовано в: : | JCI Insight |
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| Главные авторы: | , , , |
| Формат: | Artigo |
| Язык: | Inglês |
| Опубликовано: |
American Society for Clinical Investigation
2019
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| Предметы: | |
| Online-ссылка: | https://ncbi.nlm.nih.gov/pmc/articles/PMC6483501/ https://ncbi.nlm.nih.gov/pubmed/30843885 https://ncbi.nlm.nih.govhttp://dx.doi.org/10.1172/jci.insight.126703 |
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