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The Effect of Glycomacropeptide versus Amino Acids on Phenylalanine and Tyrosine Variability over 24 Hours in Children with PKU: A Randomized Controlled Trial

Introduction: In phenylketonuria (PKU), evidence suggests that casein glycomacropeptide supplemented with rate-limiting amino acids (CGMP-AA) is associated with better protein utilisation and less blood phenylalanine (Phe) variability. Aim: To study the impact of CGMP-AA on blood Phe variability usi...

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Publicado en:Nutrients
Autores principales: Daly, Anne, Evans, Sharon, Chahal, Satnam, Santra, Saikat, Pinto, Alex, Gingell, Cerys, Rocha, Júlio César, van Spronsen, Francjan, Jackson, Richard, MacDonald, Anita
Formato: Artigo
Lenguaje:Inglês
Publicado: MDPI 2019
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Acceso en línea:https://ncbi.nlm.nih.gov/pmc/articles/PMC6471794/
https://ncbi.nlm.nih.gov/pubmed/30823411
https://ncbi.nlm.nih.govhttp://dx.doi.org/10.3390/nu11030520
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