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Successful liver transplantation in common variable immune deficiency with reversal of hepatopulmonary syndrome

Common variable immune deficiency (CVID) is a primary immunodeficiency disorder that is associated with abnormal liver function tests, however advanced liver disease is uncommon. Hepatopulmonary syndrome (HPS) is a rare but debilitating complication of CVID-associated liver disease. We report a case...

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Pubblicato in:BMJ Case Rep
Autori principali: Apostolov, Ross, Sinclair, Marie, Lokan, Julie, Angus, Peter
Natura: Artigo
Lingua:Inglês
Pubblicazione: BMJ Publishing Group 2019
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Accesso online:https://ncbi.nlm.nih.gov/pmc/articles/PMC6453370/
https://ncbi.nlm.nih.gov/pubmed/30948390
https://ncbi.nlm.nih.govhttp://dx.doi.org/10.1136/bcr-2018-226095
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