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Osteomyelitis of the mandible secondary to malignant infantile osteopetrosis in an adult

Malignant infantile osteopetrosis (MIOP), an autosomal-recessive disorder, is extremely rare, presenting early in life with extreme sclerosis of the skeleton and reduced activity of osteoclasts. It was first described by Albers Schonberg in 1904. Disease manifestations include compensatory extramedu...

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Detalhes bibliográficos
Publicado no:BMJ Case Rep
Main Authors: Dunphy, Louise, Warfield, Adrian, Williams, Rhodri
Formato: Artigo
Idioma:Inglês
Publicado em: BMJ Publishing Group 2019
Assuntos:
Acesso em linha:https://ncbi.nlm.nih.gov/pmc/articles/PMC6453288/
https://ncbi.nlm.nih.gov/pubmed/30898950
https://ncbi.nlm.nih.govhttp://dx.doi.org/10.1136/bcr-2018-224452
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