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Osteomyelitis of the mandible secondary to malignant infantile osteopetrosis in an adult
Malignant infantile osteopetrosis (MIOP), an autosomal-recessive disorder, is extremely rare, presenting early in life with extreme sclerosis of the skeleton and reduced activity of osteoclasts. It was first described by Albers Schonberg in 1904. Disease manifestations include compensatory extramedu...
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Publicado no: | BMJ Case Rep |
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Main Authors: | , , |
Formato: | Artigo |
Idioma: | Inglês |
Publicado em: |
BMJ Publishing Group
2019
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Assuntos: | |
Acesso em linha: | https://ncbi.nlm.nih.gov/pmc/articles/PMC6453288/ https://ncbi.nlm.nih.gov/pubmed/30898950 https://ncbi.nlm.nih.govhttp://dx.doi.org/10.1136/bcr-2018-224452 |
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