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An adult case of atypical familial Mediterranean fever (pyrin‐associated autoinflammatory disease) similar to adult‐onset Still’s disease

We present a 55‐year‐old woman with periodic fever and symptoms similar to adult‐onset Still's disease (AOSD). She had a heterogeneous mutation of the MEFV gene and colchicine was effective. Atypical familial Mediterranean fever (pyrin‐associated autoinflammatory disease) should be considered i...

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Publicado en:Clin Case Rep
Autores principales: Tsuruma, Hayato, Sato, Hiroe, Hasegawa, Eriko, Nozawa, Yukiko, Nakatsue, Takeshi, Wada, Yoko, Kuroda, Takeshi, Suzuki, Yoshiki, Nakano, Masaaki, Narita, Ichiei
Formato: Artigo
Lenguaje:Inglês
Publicado: John Wiley and Sons Inc. 2019
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Acceso en línea:https://ncbi.nlm.nih.gov/pmc/articles/PMC6452483/
https://ncbi.nlm.nih.gov/pubmed/30997089
https://ncbi.nlm.nih.govhttp://dx.doi.org/10.1002/ccr3.2102
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