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Biallelic mutations in FDXR cause neurodegeneration associated with inflammation

Mitochondrial dysfunction lies behind many neurodegenerative disorders, due largely to the intense energy requirements of most neurons. Such mitochondrial dysfunction may work through a variety of mechanisms, from direct disruption of the electron transport chain to abnormal mitochondrial biogenesis...

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Dettagli Bibliografici
Pubblicato in:J Hum Genet
Autori principali: Slone, Jesse, Peng, Yanyan, Chamberlin, Adam, Harris, Belinda, Kaylor, Julie, McDonald, Marie T., Lemmon, Monica, El-Dairi, Mays Antonine, Tchapyjnikov, Dmitry, Gonzalez-Krellwitz, Laura A, Sellars, Elizabeth A., McConkie-Rosell, Allyn, Reinholdt, Laura G., Huang, Taosheng
Natura: Artigo
Lingua:Inglês
Pubblicazione: 2018
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Accesso online:https://ncbi.nlm.nih.gov/pmc/articles/PMC6451867/
https://ncbi.nlm.nih.gov/pubmed/30250212
https://ncbi.nlm.nih.govhttp://dx.doi.org/10.1038/s10038-018-0515-y
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