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A case of desmoplakin mutation and delayed arrhythmogenic right ventricular cardiomyopathy/dysplasia after atrial septal defect closure

Arrhythmogenic right ventricular cardiomyopathy/dysplasia (ARVC/D) is a slow-developing cardiomyopathy characterized by ventricular arrhythmias and fibrofatty replacement of the right ventricular (RV) myocardium. Its clinical diagnosis is challenging because of its variable clinical presentation and...

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Опубликовано в: :J Cardiol Cases
Главные авторы: Yoshida, Ayano, Suzuki, Atsushi, Kawada, Erisa, Tobita, Takashige, Serizawa, Naoki, Suzuki, Tsuyoshi, Arai, Kotaro, Shiga, Tsuyoshi, Shoda, Morio, Yosizawa, Saeko, Uto, Kenta, Masui, Kenta, Hagiwara, Nobuhisa
Формат: Artigo
Язык:Inglês
Опубликовано: Japanese College of Cardiology 2019
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Online-ссылка:https://ncbi.nlm.nih.gov/pmc/articles/PMC6451054/
https://ncbi.nlm.nih.gov/pubmed/30996754
https://ncbi.nlm.nih.govhttp://dx.doi.org/10.1016/j.jccase.2018.09.005
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