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Diamond Blackfan Anemia: Genetics, Pathogenesis, Diagnosis and Treatment

Diamond Blackfan Anaemia (DBA) is a sporadic inherited anemia with broad spectrum of anomalies that are presented soon after delivery. It is inherited mainly in autosomal dominant inheritance manner and caused by mutations and deletions in either large or small ribosomal protein genes that results i...

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Detalhes bibliográficos
Publicado no:EJIFCC
Main Authors: Engidaye, Getabalew, Melku, Mulugeta, Enawgaw, Bamlaku
Formato: Artigo
Idioma:Inglês
Publicado em: The Communications and Publications Division (CPD) of the IFCC 2019
Assuntos:
Acesso em linha:https://ncbi.nlm.nih.gov/pmc/articles/PMC6416817/
https://ncbi.nlm.nih.gov/pubmed/30881276
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