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Pulmonary arterial hypertension in connective tissue disorders: Pathophysiology and treatment

Pulmonary arterial hypertension (PAH) is a serious complication of connective tissue disorders (CTDs), and CTD-PAH is the second cause of PAH after the idiopathic form. PAH is characterized by increased pulmonary arterial pressure and pulmonary vascular resistance, which can lead to right heart fail...

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Библиографические подробности
Опубликовано в: :Exp Biol Med (Maywood)
Главные авторы: Zanatta, Elisabetta, Polito, Pamela, Famoso, Giulia, Larosa, Maddalena, De Zorzi, Elena, Scarpieri, Elena, Cozzi, Franco, Doria, Andrea
Формат: Artigo
Язык:Inglês
Опубликовано: SAGE Publications 2019
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Online-ссылка:https://ncbi.nlm.nih.gov/pmc/articles/PMC6405825/
https://ncbi.nlm.nih.gov/pubmed/30669861
https://ncbi.nlm.nih.govhttp://dx.doi.org/10.1177/1535370218824101
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