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Effects of long-term cysteamine treatment in patients with cystinosis

Cystinosis is a rare autosomal-recessive lysosomal storage disease with high morbidity and mortality. It is caused by mutations in the CTNS gene that encodes the cystine transporter, cystinosin, which leads to lysosomal cystine accumulation. Patients with infantile nephropathic cystinosis, the most...

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Vydáno v:Pediatr Nephrol
Hlavní autoři: Ariceta, Gema, Giordano, Vincenzo, Santos, Fernando
Médium: Artigo
Jazyk:Inglês
Vydáno: Springer Berlin Heidelberg 2017
Témata:
On-line přístup:https://ncbi.nlm.nih.gov/pmc/articles/PMC6394685/
https://ncbi.nlm.nih.gov/pubmed/29260317
https://ncbi.nlm.nih.govhttp://dx.doi.org/10.1007/s00467-017-3856-4
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