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Biochemistry of Autoinflammatory Diseases: Catalyzing Monogenic Disease

Monogenic autoinflammatory disorders are a group of conditions defined by systemic or localized inflammation without identifiable causes, such as infection. In contrast to classical primary immunodeficiencies that manifest with impaired immune responses, these disorders are due to defects in genes t...

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Détails bibliographiques
Publié dans:Front Immunol
Auteurs principaux: Beck, David B., Aksentijevich, Ivona
Format: Artigo
Langue:Inglês
Publié: Frontiers Media S.A. 2019
Sujets:
Accès en ligne:https://ncbi.nlm.nih.gov/pmc/articles/PMC6365650/
https://ncbi.nlm.nih.gov/pubmed/30766537
https://ncbi.nlm.nih.govhttp://dx.doi.org/10.3389/fimmu.2019.00101
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