Carregant...

Reductions in ATPase activity, actin sliding velocity, and myofibril stability yield muscle dysfunction in Drosophila models of myosin-based Freeman–Sheldon syndrome

Using Drosophila melanogaster, we created the first animal models for myosin-based Freeman–Sheldon syndrome (FSS), a dominant form of distal arthrogryposis defined by congenital facial and distal skeletal muscle contractures. Electron microscopy of homozygous mutant indirect flight muscles showed no...

Descripció completa

Guardat en:
Dades bibliogràfiques
Publicat a:Mol Biol Cell
Autors principals: Rao, Deepti S., Kronert, William A., Guo, Yiming, Hsu, Karen H., Sarsoza, Floyd, Bernstein, Sanford I.
Format: Artigo
Idioma:Inglês
Publicat: The American Society for Cell Biology 2019
Matèries:
Accés en línia:https://ncbi.nlm.nih.gov/pmc/articles/PMC6337914/
https://ncbi.nlm.nih.gov/pubmed/30379605
https://ncbi.nlm.nih.govhttp://dx.doi.org/10.1091/mbc.E18-08-0526
Etiquetes: Afegir etiqueta
Sense etiquetes, Sigues el primer a etiquetar aquest registre!