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Feeding Difficulties and Orofacial Myofunctional Disorder in Patients with Hepatic Glycogen Storage Diseases

Hepatic glycogen storage diseases (GSDs) are inborn errors of metabolism whose dietary treatment involves uncooked cornstarch administration and restriction of simple carbohydrate intake. The prevalence of feeding difficulties (FDs) and orofacial myofunctional disorders (OMDs) in these patients is u...

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Detalhes bibliográficos
Publicado no:JIMD Rep
Main Authors: Martinez, Chenia Caldeira, Tonon, Tássia, Nalin, Tatiéle, Refosco, Lilia Farret, de Souza, Carolina Fischinger Moura, Schwartz, Ida Vanessa Doederlein
Formato: Artigo
Idioma:Inglês
Publicado em: Springer Berlin Heidelberg 2018
Assuntos:
Acesso em linha:https://ncbi.nlm.nih.gov/pmc/articles/PMC6336547/
https://ncbi.nlm.nih.gov/pubmed/30242630
https://ncbi.nlm.nih.govhttp://dx.doi.org/10.1007/8904_2018_131
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