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Hepatomegaly and type 1 diabetes: a clinical case of Mauriac’s syndrome

BACKGROUND: Hepatic glycogenosis is characterized by excessive glycogen accumulation in hepatocytes and represents a complication of poor controlled type 1 diabetes. It can be caused by excessive insulin doses or recurrent ketoacidosis episodes. Mauriac’s syndrome is a rare disease, which includes s...

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Detalhes bibliográficos
Publicado no:Ital J Pediatr
Main Authors: Lombardo, Fortunato, Passanisi, Stefano, Gasbarro, Albino, Tuccari, Giovanni, Ieni, Antonio, Salzano, Giuseppina
Formato: Artigo
Idioma:Inglês
Publicado em: BioMed Central 2019
Assuntos:
Acesso em linha:https://ncbi.nlm.nih.gov/pmc/articles/PMC6322227/
https://ncbi.nlm.nih.gov/pubmed/30616577
https://ncbi.nlm.nih.govhttp://dx.doi.org/10.1186/s13052-018-0598-2
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