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Anti-MDA5 Antibody-positive Dermatomyositis Complicated by Autoimmune-associated Hemophagocytic Syndrome That Was Successfully Treated with Immunosuppressive Therapy and Plasmapheresis

A 56-year-old Japanese woman with muscle weakness, increased creatine kinase and aldolase levels, and characteristic cutaneous lesions was diagnosed with anti-melanoma differentiation-associated gene 5 antibody (anti-MDA5 antibody)-positive dermatomyositis. She also had interstitial lung disease (IL...

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Detalhes bibliográficos
Publicado no:Intern Med
Main Authors: Fujita, Yuya, Fukui, Shoichi, Suzuki, Takahisa, Ishida, Midori, Endo, Yushiro, Tsuji, Sousuke, Takatani, Ayuko, Igawa, Takashi, Shimizu, Toshimasa, Umeda, Masataka, Sumiyoshi, Remi, Nishino, Ayako, Koga, Tomohiro, Kawashiri, Shin-ya, Iwamoto, Naoki, Ichinose, Kunihiro, Tamai, Mami, Nakamura, Hideki, Origuchi, Tomoki, Abe, Kuniko, Kawakami, Atsushi
Formato: Artigo
Idioma:Inglês
Publicado em: The Japanese Society of Internal Medicine 2018
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Acesso em linha:https://ncbi.nlm.nih.gov/pmc/articles/PMC6306524/
https://ncbi.nlm.nih.gov/pubmed/29984753
https://ncbi.nlm.nih.govhttp://dx.doi.org/10.2169/internalmedicine.1121-18
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