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Aberrant IP(3) receptor activities revealed by comprehensive analysis of pathological mutations causing spinocerebellar ataxia 29

Spinocerebellar ataxia type 29 (SCA29) is autosomal dominant congenital ataxia characterized by early-onset motor delay, hypotonia, and gait ataxia. Recently, heterozygous missense mutations in an intracellular Ca(2+) channel, inositol 1,4,5-trisphosphate (IP(3)) receptor type 1 (IP(3)R1), were iden...

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Vydáno v:Proc Natl Acad Sci U S A
Hlavní autoři: Ando, Hideaki, Hirose, Matsumi, Mikoshiba, Katsuhiko
Médium: Artigo
Jazyk:Inglês
Vydáno: National Academy of Sciences 2018
Témata:
On-line přístup:https://ncbi.nlm.nih.gov/pmc/articles/PMC6275503/
https://ncbi.nlm.nih.gov/pubmed/30429331
https://ncbi.nlm.nih.govhttp://dx.doi.org/10.1073/pnas.1811129115
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