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Severe Familial Hypertriglyceridemia: Successful Treatment With Insulin and a Modified Meal Plan

CONTEXT: Mutations in genes encoding the lipoprotein lipase enzyme, its cofactor, or transport proteins can cause severe familial hypertriglyceridemia, resulting in serious complications, such as severe pancreatitis, hepatosplenomegaly, lipid encephalopathy, and failure to thrive. Current treatment...

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Detalles Bibliográficos
Publicado en:J Endocr Soc
Autores principales: Ayyavoo, Ahila, Raghupathy, Palany, Agarwal, Meenal, Hofman, Paul
Formato: Artigo
Lenguaje:Inglês
Publicado: Endocrine Society 2018
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Acceso en línea:https://ncbi.nlm.nih.gov/pmc/articles/PMC6270957/
https://ncbi.nlm.nih.gov/pubmed/30519673
https://ncbi.nlm.nih.govhttp://dx.doi.org/10.1210/js.2018-00299
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