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An autoantibody identifies arrhythmogenic right ventricular cardiomyopathy and participates in its pathogenesis

AIMS: Arrhythmogenic right ventricular cardiomyopathy (ARVC) is characterized by right ventricular myocardial replacement and life-threatening ventricular arrhythmias. Desmosomal gene mutations are sometimes identified, but clinical and genetic diagnosis remains challenging. Desmosomal skin disorder...

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Wedi'i Gadw mewn:
Manylion Llyfryddiaeth
Cyhoeddwyd yn:Eur Heart J
Prif Awduron: Chatterjee, Diptendu, Fatah, Meena, Akdis, Deniz, Spears, Danna A, Koopmann, Tamara T, Mittal, Kirti, Rafiq, Muhammad A, Cattanach, Bruce M, Zhao, Qili, Healey, Jeff S, Ackerman, Michael J, Bos, Johan Martijn, Sun, Yu, Maynes, Jason T, Brunckhorst, Corinna, Medeiros-Domingo, Argelia, Duru, Firat, Saguner, Ardan M, Hamilton, Robert M
Fformat: Artigo
Iaith:Inglês
Cyhoeddwyd: Oxford University Press 2018
Pynciau:
Mynediad Ar-lein:https://ncbi.nlm.nih.gov/pmc/articles/PMC6247665/
https://ncbi.nlm.nih.gov/pubmed/30239670
https://ncbi.nlm.nih.govhttp://dx.doi.org/10.1093/eurheartj/ehy567
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