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CT findings in pulmonary alveolar proteinosis: serial changes and prognostic implications

BACKGROUND: Pulmonary alveolar proteinosis (PAP) is a rare disease of unknown origin, characterized by impaired surfactant metabolism. In some patients, residual disease is observed after treatment; notably, this may progress to end-stage pulmonary fibrosis. This study was performed to evaluate chan...

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Dettagli Bibliografici
Pubblicato in:J Thorac Dis
Autori principali: Da Nam, Bo, Kim, Tae Jung, Chung, Man Pyo, Chung, Myung Jin, Kim, Tae Sung, Lee, Kyung Soo
Natura: Artigo
Lingua:Inglês
Pubblicazione: AME Publishing Company 2018
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Accesso online:https://ncbi.nlm.nih.gov/pmc/articles/PMC6236152/
https://ncbi.nlm.nih.gov/pubmed/30505485
https://ncbi.nlm.nih.govhttp://dx.doi.org/10.21037/jtd.2018.09.86
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