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Pulmonary Manifestations in Tuberous Sclerosis Complex

Tuberous sclerosis complex has manifestations in many organ systems, including brain, heart, kidney, skin, and lung. The primary manifestations in the lung are lymphangioleiomyomatosis (LAM) and multifocal micronodular pneumocyte hyperplasia (MMPH). LAM affects almost exclusively women, and causes c...

Deskribapen osoa

Gorde:
Xehetasun bibliografikoak
Argitaratua izan da:Am J Med Genet C Semin Med Genet
Egile Nagusiak: Gupta, Nishant, Henske, Elizabeth P.
Formatua: Artigo
Hizkuntza:Inglês
Argitaratua: 2018
Gaiak:
Sarrera elektronikoa:https://ncbi.nlm.nih.gov/pmc/articles/PMC6209521/
https://ncbi.nlm.nih.gov/pubmed/30055039
https://ncbi.nlm.nih.govhttp://dx.doi.org/10.1002/ajmg.c.31638
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